Dandy–Walker malformation
CONGENITAL DISORDER OF NERVOUS SYSTEM
Dandy Walker syndrome; Dandy-Walker malformation; Dandy-Walker cyst; Dandy-Walker deformity; Luschka-Magendie foramina atresia; Dandy-walker syndrome; Dandy Walker complex; Dandy walker complex; Dandy Walker malformation; Dandy-Walker syndrome; Dandy walker; Dandy-walker; Dandy–Walker syndrome; Dandy–Walker variant; Dandy–Walker complex; Dandy-Walker variant; Dandy-Walker complex; Dandy–Walker continuum; Dandy-Walker continuum; Mega cisterna magna; Mega–cisterna magna; Megacisterna magna; Mega-cisterna magna
Dandy–Walker malformation (DWM), also known as Dandy–Walker syndrome (DWS), is a rare congenital brain malformation in which the part joining the two hemispheres of the cerebellum (the cerebellar vermis) does not fully form, and the fourth ventricle and space behind the cerebellum (the posterior fossa) are enlarged with cerebrospinal fluid. Most of those affected develop hydrocephalus within the first year of life, which can present as increasing head size, vomiting, excessive sleepiness, irritability, downward deviation of the eyes and seizures.